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Familial Pseudocoarctation of the Aorta.

Summary of "Familial Pseudocoarctation of the Aorta."

Pseudocoarctation of the aorta (PCOA) is an unusual congenital malformation of the aortic arch characterized by an acute anterior angulation of the aortic arch at the level of the ligamentum arteriosum with little or no obstruction. This report describes the occurrence of PCOA and other aortic arch abnormalities including true coarctation, right aortic arch, and aneurysms of the proximal and distal aortic arch in three generations of a single family. To our knowledge, a familial form of PCOA has not been described.

Affiliation

Department of Diagnostic Imaging, Rhode Island Hospital, Warren Alpert School of Medicine of Brown University, Providence, RI, 02903, USA.

Journal Details

This article was published in the following journal.

Name: Pediatric cardiology
ISSN: 1432-1971
Pages:

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