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Long-term survival with cloacal dysgenesis sequence.

06:00 EST 16th December 2011 | BioPortfolio

Summary of "Long-term survival with cloacal dysgenesis sequence."

Cloacal dysgenesis sequence (CDS) is a rare and lethal malformation. We report such a case of long-term survival, currently to 12 years of age. In the fetal period, she received a timely placement of vesico-amniotic shunt for a megabladder due to a severe urethral obstruction. Postnatally, cystostomy and colostomy were created because of no perineal opening of urethra, vagina, and anus. Anorectoplasty, construction of efferent conduit, and colostomy closure were performed at 4 years of age. Ileovaginoplasty and ileovesicostomy which was a Mitrofanoff-type of conduit, and labioplasty were performed at the age of 11 years. To the best of our knowledge, only five survivors with CDS over 1 year of age have been reported.

Affiliation

Department of Pediatric Surgery, Ibaraki Children's Hospital, 3-3-1 Futabadai, Mito-city, Ibaraki, 311-4145, Japan, to.yanai@ibaraki-kodomo.com.

Journal Details

This article was published in the following journal.

Name: Pediatric surgery international
ISSN: 1437-9813
Pages:

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Pediatrics is the general medicine of childhood. Because of the developmental processes (psychological and physical) of childhood, the involvement of parents, and the social management of conditions at home and at school, pediatrics is a specialty. With ...


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