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Long-term survival with cloacal dysgenesis sequence.

01:23 EDT 31st July 2014 | BioPortfolio

Summary of "Long-term survival with cloacal dysgenesis sequence."

Cloacal dysgenesis sequence (CDS) is a rare and lethal malformation. We report such a case of long-term survival, currently to 12 years of age. In the fetal period, she received a timely placement of vesico-amniotic shunt for a megabladder due to a severe urethral obstruction. Postnatally, cystostomy and colostomy were created because of no perineal opening of urethra, vagina, and anus. Anorectoplasty, construction of efferent conduit, and colostomy closure were performed at 4 years of age. Ileovaginoplasty and ileovesicostomy which was a Mitrofanoff-type of conduit, and labioplasty were performed at the age of 11 years. To the best of our knowledge, only five survivors with CDS over 1 year of age have been reported.

Affiliation

Department of Pediatric Surgery, Ibaraki Children's Hospital, 3-3-1 Futabadai, Mito-city, Ibaraki, 311-4145, Japan, to.yanai@ibaraki-kodomo.com.

Journal Details

This article was published in the following journal.

Name: Pediatric surgery international
ISSN: 1437-9813
Pages:

Links

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