Electrophysiological study with prophylactic pacing and survival in adults with myotonic dystrophy and conduction system disease.

06:00 EDT 29th March 2012 | BioPortfolio

Summary of "Electrophysiological study with prophylactic pacing and survival in adults with myotonic dystrophy and conduction system disease."

Up to one-third of patients with myotonic dystrophy type 1 die suddenly. Thus far, no intervention has effectively prevented sudden death.


Pierre et Marie Curie-Paris 6 University, Myology Institute, Pitié-Salpêtrière Hospital, 75013 Paris, France. karim.wahbi@cch.aphp.fr

Journal Details

This article was published in the following journal.

Name: JAMA : the journal of the American Medical Association
ISSN: 1538-3598
Pages: 1292-301


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