Idiopathic Orbital Inflammation Leading to Unilateral Blindness Over a 2-Day Presentation in a Child.

18:23 EDT 1st October 2014 | BioPortfolio

Summary of "Idiopathic Orbital Inflammation Leading to Unilateral Blindness Over a 2-Day Presentation in a Child."

An 8-year-old boy developed vision loss to no light perception on the left side over a 2-day period. He initially presented with unilateral eyelid swelling, which progressed to bilateral edema and an eventual left-sided orbital apex syndrome. Orbital imaging revealed enlarged extraocular muscles, and biopsy confirmed idiopathic orbital inflammation. Despite subsequent orbital decompression, high-dose steroids, and additional steroid-sparing therapy, he did not regain vision after 9 months of follow up.

Affiliation

*Scheie Eye Institute, University of Pennsylvania School of Medicine; †Department of Pathology and Laboratory Medicine, Children's Hospital of Philadelphia; and ‡Department of Ophthalmology, Children's Hospital of Philadelphia, University of Pennsylva

Journal Details

This article was published in the following journal.

Name: Ophthalmic plastic and reconstructive surgery
ISSN: 1537-2677
Pages:

Links

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Medical and Biotech [MESH] Definitions

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