Case for diagnosis. Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder.

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Summary of "Case for diagnosis. Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder."

Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder is a rare disease, with an indolent evolution and benign course. The classic presentation is a solitary nodule on the face or trunk. The disorder's rarity and clinical and histopathological characteristics, can make the diagnosis difficult. We present the case of a 36-year-old Caucasian woman with a purplish erythematous nodule, hardened, shiny, asymptomatic, on the left nasal ala, which had grown progressively for 45 days. Histopathological examination and immunohistochemistry panel demonstrated alterations consistent with primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder. There was complete remission of the condition within 60 days of treatment with potent occlusive corticosteroids.


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This article was published in the following journal.

Name: Anais brasileiros de dermatologia
ISSN: 1806-4841
Pages: 99-101


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