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Hydranencephaly complicated by central diabetes insipidus: report of two cases and systematic review of literature.

08:00 EDT 30th March 2019 | BioPortfolio

Summary of "Hydranencephaly complicated by central diabetes insipidus: report of two cases and systematic review of literature."

Hydranencephaly is a congenital condition characterized by the complete or near-complete absence of the cerebral cortex and basal ganglia, while central diabetes insipidus (CDI) is a condition characterized by the inability to concentrate urine due to a deficiency in antidiuretic hormone (ADH). CDI is known to occur in midline congenital malformations such as holoprosencephaly and septo-optic dysplasia, but its association with hydranencephaly is less well-established.

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Name: Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
ISSN: 1433-0350
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